| Minimum | Maximum | Mean (SD) |
---|---|---|---|
Age of onset (years) | 0.50 | 13.00 | 5.83 (4.15) |
Disease duration (years) | 0.50 | 12.00 | 3.98 (3.17) |
Frequency of hospital admissions per year | 1.00 | 7.00 | 2.28 (1.75) |
MRC dyspnea score | .00 | 5.00 | 2.05 (1.65) |
ILD severity score | 2.00 | 5.00 | 2.80 (1.09) |
HRCT score | .00 | 3.00 | 1.85 (0.92) |
Respiratory rate (breath/minute) | 15.00 | 78.00 | 35.30 (16.53) |
Heart rate (pulse/minute) | 85.00 | 140.00 | 102.53 (14.52) |
Oxygen saturation (%) | 68.00 | 99.00 | 93.75 (7.22) |
FEV1 (% of predicted) | 24.80 | 77.20 | 53.66 (14.42) |
FVC (% of predicted) | 26.80 | 75.40 | 57.37 (11.99) |
FEV1/FVC ratio (% of predicted) | 55.00 | 111.40 | 91.64 (16.22) |
DLCO-SB (% of predicted) | 27.90 | 82.10 | 61.72 (21.76) |
Total leukocyte count (× 103/μl) | 3.30 | 26.80 | 9.70 (5.44) |
Hemoglobin (g/dl) | 7.90 | 14.20 | 11.77 (1.63) |
Platelets count (× 103/μl) | 171.00 | 717.00 | 366.80 (143.32) |