Demographic data | Patient 1 | Patient 2 |
---|---|---|
Age (years) | 12 | 7 |
Sex | Female | Female |
Age of onset of symptoms (years) | 3 | 5 |
Disease duration (years) | 10 | 3 |
Frequency of hospital admission (/year) | 2 | 4 |
Exposure | Birds Cigarette smoke Fire smoke | Birds Cigarette smoke |
Symptoms | Cyanosis Dyspnea Cough Clubbing Expectoration | Cyanosis Dyspnea Cough Clubbing |
Weight for age (Z-score) | < − 3 | Between − 3 and − 2 |
Height for age (Z-score) | < − 3 | Between − 3 and − 2 |
BMI for age (Z-score) | < − 3 | Between − 3 and − 2 |
Respiratory rate (breath/min) | 53 (Tachypneic for age) | 62 (Tachypneic for age) |
Heart rate (beat/min) | 104 (Tachycardic for age) | 113 (Tachycardic for age) |
Modified MRC dyspnea score | 4 | 3 |
Chest examination | Fine and coarse crepitations | Fine crepitations |
Heart examination | Accentuated second heart sound | Normal |
Oxygen saturation at rest (%) | 92 | 93 |
ILD severity score | 5 | 4 |
Total leukocyte count (× 103/μl) | 18.7 | 26.9 |
Hemoglobin (g/dl) | 11.3 | 10.9 |
Platelets count (× 103/μl) | 392 | 369 |
Chest x-ray | Reticulonodular pattern | Reticulonodular pattern |
HRCT score | 3 | 3 |
FEV1 % of predicted | 46.4 | 59.4 |
FVC % of predicted | 50.7 | 52.7 |
FEV1/FVC | 80.92 | 111.3 |
DLCO-SB (%) | Could not be performed | Could not be performed |