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The Egyptian Journal of Bronchology
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A rare presentation of a rare disease

Egyptian Journal of Bronchology volume 8, pages 173–174 (2014)Cite this article

Abstract

Background

Castleman’s disease, a rare condition of uncertain etiology, is associated with lymphoproliferation. It is histologically and prognostically distinct from malignant lymph node hyperplasia.

Case presentation

We report a case of a female patient who presented with interstitial lung disease and mediastinal lymphadenopathy, not responding to usual treatment.

Conclusion

Definitive histological diagnosis in patients with lymphadenopathic presentation associated with systemic symptoms is important to differentiate Castleman’s disease from malignant lymphoma.

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Author information

Authors and Affiliations

  1. Department of Pulmonary Medicine, Faculty of Medicine, Ain Shams University, 147 Khalifa El Maamoun Street, Abassia Square, Cairo, 11566, Egypt

    Tamer Ibraheem MD

Authors
  1. Tamer Ibraheem MD
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Corresponding author

Correspondence to Tamer Ibraheem MD.

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Cite this article

Ibraheem, T. A rare presentation of a rare disease. Egypt J Bronchol 8, 173–174 (2014). https://doi.org/10.4103/1687-8426.145724

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  • DOI: https://doi.org/10.4103/1687-8426.145724

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